Difference between revisions of "Fibromatoses"
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*[[Familial adenomatous polyposis]].<ref name=Ref_PBoD8_1092>{{Ref PBoD8|1092}}</ref> | *[[Familial adenomatous polyposis]].<ref name=Ref_PBoD8_1092>{{Ref PBoD8|1092}}</ref> | ||
**[[Gardner syndrome]]. | **[[Gardner syndrome]]. | ||
**[[Desmoid-type fibromatosis]]. | ***[[Desmoid-type fibromatosis]]. | ||
*Hereditary desmoid syndrome. | *Hereditary desmoid syndrome. | ||
Revision as of 00:13, 22 March 2012
Fibromatoses are a group of benign stromal lesions that may be seen in pediatric pathology and may or may not be associated with syndromes.
Syndromes associated with fibromatoses
- Familial adenomatous polyposis.[1]
- Hereditary desmoid syndrome.
Microscopic
Features:
- Bland spindle cells - typically in fascicles.
- Small thin blood vessels that are parallel to one another.
- Nuclei of blood vessels are typically darker staining than those of the lesion.
DDx:
- Metaplastic carcinoma, e.g. metaplastic breast carcinoma.
- Nodular fasciitis.
See also
References
- ↑ Kumar, Vinay; Abbas, Abul K.; Fausto, Nelson; Aster, Jon (2009). Robbins and Cotran pathologic basis of disease (8th ed.). Elsevier Saunders. pp. 1092. ISBN 978-1416031215.