Difference between revisions of "Fibromatoses"
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***[[Desmoid-type fibromatosis]]. | ***[[Desmoid-type fibromatosis]]. | ||
*Hereditary desmoid syndrome. | *Hereditary desmoid syndrome. | ||
==Types== | |||
===Superficial=== | |||
*Palmar ([[Dupuytren's contracture]]). | |||
*Plantar. | |||
*Penile (Peyronie's disease). | |||
===Deep=== | |||
*[[Desmoid-type fibromatosis]]. | |||
*Fibromatosis coli. | |||
*Others. | |||
==Microscopic== | ==Microscopic== | ||
Revision as of 15:47, 20 April 2012
Fibromatoses are a group of benign stromal lesions that may be seen in pediatric pathology and may or may not be associated with syndromes.
Syndromes associated with fibromatoses
- Familial adenomatous polyposis.[1]
- Hereditary desmoid syndrome.
Types
Superficial
- Palmar (Dupuytren's contracture).
- Plantar.
- Penile (Peyronie's disease).
Deep
- Desmoid-type fibromatosis.
- Fibromatosis coli.
- Others.
Microscopic
Features:
- Bland spindle cells - typically in fascicles.
- Small thin blood vessels that are parallel to one another.
- Nuclei of blood vessels are typically darker staining than those of the lesion.
DDx:
- Metaplastic carcinoma, e.g. metaplastic breast carcinoma.
- Nodular fasciitis.
See also
References
- ↑ Kumar, Vinay; Abbas, Abul K.; Fausto, Nelson; Aster, Jon (2009). Robbins and Cotran pathologic basis of disease (8th ed.). Elsevier Saunders. pp. 1092. ISBN 978-1416031215.